Peutz-Jeghers 증후군: 증례보고와 문헌고찰
Peutz-Jeghers Syndrome: A Case Report and Review of Literature
김현수, 김성민, 최진영, 명훈, 이종호, 이석근,
소속 상세정보
김현수 ( Kim Hyun-Soo ) - 서울대학교 치의학대학원 구강악안면외과학교실
김성민 ( Kim Soung-Min ) - 서울대학교 치의학대학원 구강악안면외과학교실
최진영 ( Choi Jin-Young ) - 서울대학교 치의학대학원 구강악안면외과학교실
명훈 ( Myoung Hoon ) - 서울대학교 치의학대학원 구강악안면외과학교실
이종호 ( Lee Jong-Ho ) - 서울대학교 치의학대학원 구강악안면외과학교실
이석근 ( Lee Suk-Keun ) - 강릉원주대학교 치과대학 구강병리학교실
KMID : 0360120120340050363
Abstract
Peutz-Jeghers syndrome is a rare syndrome with characteristic features of multiple hamartomatous polyps and mucocutaneous pigmentation. This syndrome is an autosomal dominant disease, and has complications related with polyps of the gastrointestinal tract, such as small bowel obstruction, iron deficiency anemia associated with bleeding, and intussusceptions. Many studies have reported about higher cancer risk of patients with this syndrome than those with no syndrome in the gastrointestinal tract, including gastric, duodenal, jejunal and the extragastrointestinal organs, such as gallbladder, breast and reproductive system. There are guidelines for periodic test for early detection and treatment for higher risk organs. We report a case of Peutz-Jeghers syndrome patient in the emphasis of Oral and Maxillofacial surgeon’s role with review of the literature.
키워드
Peutz-Jeghers syndrome;Pigmentation;Intestinal polyposis
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